Hemophilia, an X-linked disorder, is a congenital inherited bleeding disorder of the clotting mechanism cause by an abnormal gene that produces a defective clotting factor protein with little or no clotting ability. The two most common forms of this disorder are Classic hemophilia (type A) which is caused by the lack of factor VIII and Christmas disease (type B) is caused by the deficiency in factor IX. Since both of these disorders are X-linked, the female is the carrier and the disorder is manifested only in males.
Hemophilia is classified into the following three groups, based on the severity of factor deficiency, mild (5-50%), moderate (1-5%) and severe (1%). Hemophiliacs are at risk for prolonged bleeding or hemorrhage as a result of minor trauma. Individuals with severe hemophilia, or less than 1% clotting factor, are also at risk to suffer from spontaneous bleeding without trauma or more severe prolonged bleeding after trauma. Bleeding can
occur at any part of the body. Hemarthrosis, or bleeding into the joint spaces, is the most common complication of severe hemophilia. The knee joint is the most frequent joint involved.
Nursing Care Plans
The nursing care plan goals for a client with hemophilia may include absence of complications and pain, prevention of injury and bleeding, improved physical mobility, and understanding of the disease condition and its management.
Here are five (5) nursing care plans (NCP) and nursing diagnosis for patients with hemophilia:
Compromised Family Coping
Nursing Diagnosis
- Compromised Family Coping
May be related to
- Inadequate or incorrect information or understanding
- Prolonged disease or disability progression that exhausts the physical and emotional supportive capacity of caretakers
Possibly evidenced by
- Expression and/or confirmation of concern and inadequate knowledge about long-term care needs, problems, and complications,
- Anxiety and guilt
- Overprotection of child
Desired Outcomes
- Family will cope effectively with child’s illness.
| Nursing Interventions | Rationale |
|---|---|
| Assess family’s coping methods and their effectiveness; family interactions and expectations related to long-term care, developmental level of family; response of siblings; knowledge and use of support systems and resources; presence of guilt and anxiety; overprotection and/or overindulgent behaviors. |
Identifies coping methods that work and the need to utilize new coping skills and behaviors, family attitudes; child with special long-term needs either strengthen or distort family relationships and an undue degree of overprotection may be detrimental to child’s growth and development such as disallowing school attendance or peer activities, avoiding discipline of child, and disallowing child to assume responsibility for ADL. |
| Encourage family members to verbalize problem areas and develop solutions on their own. | Decreases anxiety and enhances understanding; provides family an opportunity to recognize problems and create problem-solving strategies. |
| Encourage family members to express feelings, such as how they deal with the chronic needs of a family member and coping patterns that help or hinder adjustment to the problems. |
Allows for venting of feelings, which relieves guilt and anxiety and helps determine need for information and support. |
| Assist family in setting short- and long-term goals for the child and integrate child into family activities, include participation of all family. | Promotes involvement and control over situations and maintains the role of family members and parents. |
| Provide information about long-term care and management. | Enhances family understanding of medical regimen and responsibilities of family members. |
| Inform family that overprotective behavior may hinder growth and development and that child should be treated as normally as possible. |
Promotes understanding of the importance of making child one of the family and the adverse effects of overprotection of the child. |
| Provide assistance of social worker, counselor, or other as needed. |
Gives support to the family faced with long-term care of a child with a serious illness. |
See Also
You may also like the following posts and care plans:
- Nursing Care Plan: The Ultimate Guide and Database – the ultimate database of nursing care plans for different diseases and conditions! Get the complete list!
- Nursing Diagnosis: The Complete Guide and List – archive of different nursing diagnoses with their definition, related factors, goals and nursing interventions with rationale.
Hematologic and Lymphatic Care Plans
Care plans related to the hematologic and lymphatic system:
- Anaphylactic Shock | 4 Care Plans
- Anemia | 4 Care Plans
- Aortic Aneurysm | 4 Care Plans
- Deep Vein Thrombosis | 5 Care Plans
- Disseminated Intravascular Coagulation | 4 Care Plans
- Hemophilia | 5 Care Plans
- Leukemia | 5 Care Plans
- Lymphoma | 3 Care Plans
- Sepsis and Septicemia | 6 Care Plans
- Sickle Cell Anemia Crisis | 6 Care Plans